KIMS doctors treat rare liver disease

Metro India News | Hyderabad 

Doctors at KIMS Hospitals successfully treated a 26-year-old woman suffering from an extremely rare and life-threatening liver complication caused by Weber-Christian Disease, without performing a liver transplant, despite medical criteria indicating an urgent need for transplantation.

According to Dr. Sarath Chandra Mouli Veeravalli, Clinical Director, Department of Rheumatology and Clinical Immunology and Dr. K.N. Chandan Kumar, Director, Hepatology and Transplant Hepatology, the patient’s condition represented rare case reported worldwide.

The patient, a resident of Hyderabad, was first diagnosed with the condition in 2018 after presenting with painful nodules on her hands and legs along with recurrent fever. Recently, she was brought to KIMS Hospitals in critical condition.

Doctors noted that she fulfilled the internationally accepted King’s College Criteria for emergency liver transplantation.  The patient was treated with pulse steroids, and advanced immunomodulatory therapy. This marked the first-ever reported use of Anakunra in the world to treat Weber-Christian Disease with fulminant hepatic failure.

She is currently leading a normal life and remains under regular medical follow-up. The doctors stated that early recognition of rare autoimmune disorders, rapid multidisciplinary coordination, and the use of targeted immunotherapy played a key role in saving the patient’s life.